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Confidence Scores

What the Confidence Score Means

Each variant receives a continuous confidence score alongside its ACMG classification. The score reflects how far the variant's Bayesian point total is from the nearest classification boundary -- higher values indicate that the classification is well-supported by the available evidence.

Score Ranges

ClassificationPoint RangeConfidenceInterpretation
Pathogenic>= 100.80-0.99Higher points = higher confidence
Likely Pathogenic6-90.70-0.90Closer to 10 = higher confidence
VUS0-50.30-0.60Near boundaries = may reclassify with additional evidence
Likely Benign-1 to -50.70-0.90Closer to -6 = higher confidence
Benign<= -60.80-0.99Lower points = higher confidence

How to Interpret

The confidence score is derived from the distance between the variant's point total and the nearest classification boundary. A Pathogenic variant with 15 points has higher confidence than one with exactly 10 points, because the 15-point variant would need more contradictory evidence to be reclassified.

VUS variants near the Likely Pathogenic boundary (5 points) are particularly important to note -- a single additional Supporting pathogenic criterion would reclassify them. These are high-priority candidates for additional evidence gathering (functional studies, family segregation, updated ClinVar review).

Important Note

The confidence score reflects classification evidence strength, not the probability of disease causation. A high-confidence Pathogenic classification means the evidence strongly supports pathogenicity under the ACMG framework, but clinical significance still depends on the patient's phenotype, inheritance pattern, and clinical context.