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Understanding Results

Results Organization

Results are organized by gene, not by individual variant. Each gene card shows a summary of the most clinically relevant variant in that gene. Expanding the card reveals all individual variants with their complete annotation data. This gene-centric view helps the geneticist focus on the biological context rather than individual base changes.

Variant Annotations

Each variant displays the following fields. Together, these provide the evidence a geneticist needs to assess clinical relevance.

ACMG Classification

Pathogenic, Likely Pathogenic, VUS, Likely Benign, or Benign. Determined by the Bayesian point system.

ACMG Criteria

Which specific criteria were triggered (e.g., PVS1, PM2, PP3_Strong) and their evidence strength levels.

Confidence Score

A continuous score reflecting the strength of classification evidence. Higher values indicate greater confidence in the classification.

Consequence

The predicted effect on the transcript: frameshift, missense, synonymous, splice donor, stop gained, and others.

Impact

Severity classification from Ensembl VEP: HIGH, MODERATE, LOW, or MODIFIER.

HGVS Notation

Standardized variant description at genomic (g.), coding (c.), and protein (p.) levels.

Genotype

Heterozygous (0/1), homozygous alternate (1/1), or hemizygous. Indicates the number of copies of the variant allele.

Population Frequency

gnomAD global allele frequency and population-specific maximum frequency. Lower frequency generally indicates higher clinical relevance.

ClinVar Significance

What ClinVar reports for this variant, with the review star level indicating assertion quality.

Computational Predictors

BayesDel score (used in classification) plus display predictors: SIFT, AlphaMissense, MetaSVM, DANN, PhyloP, GERP.

SpliceAI Scores

Four delta scores predicting splice impact: acceptor gain, acceptor loss, donor gain, donor loss.

Gene Constraint

pLI, LOEUF, and observed/expected loss-of-function ratio. Indicates how tolerant the gene is to damaging variation.

HPO Associations

Which clinical phenotypes are associated with this gene in the HPO database.

Phenotype Match Score

How well this gene matches the patient presentation (0-100), if HPO terms were provided.

Screening Tier

Tier 1 through 4 priority classification based on multi-dimensional scoring.

Literature Evidence

Relevant publications from the local PubMed database, ranked by clinical relevance.

What Each ACMG Classification Means

ClassificationClinical MeaningAction
PathogenicVariant causes disease.Report to clinician.
Likely PathogenicStrong evidence variant causes disease (>90% certainty per ACMG).Report to clinician.
VUSInsufficient evidence to classify.May require additional evidence gathering.
Likely BenignStrong evidence variant does not cause disease.Generally not reported.
BenignVariant does not cause disease.Not reported.

Where to Start

The Screening Tier 1 list provides the highest-priority variants based on classification strength, phenotype correlation, population rarity, and gene constraint. Start there. If Tier 1 does not explain the clinical presentation, proceed to Tier 2 and consider additional evidence gathering for VUS candidates with strong phenotype matches.

For details on how screening tiers are assigned, see Screening Tier System. For classification methodology, see the full Methodology page.