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Documentation / Classification / ClinVar Integration

ClinVar Integration

Three Uses of ClinVar Data

As evidence criteria

PS1 (strong, 2+ stars), PP5 (supporting, 1 star), BP6 (supporting, 1+ star). ClinVar assertions contribute to the Bayesian point total alongside all other criteria.

As classification override

When no conflicting computational evidence exists, ClinVar assertions with sufficient review stars can determine the final classification directly.

As quality filter rescue

ClinVar Pathogenic/Likely Pathogenic variants are never discarded by quality filtering, regardless of sequencing quality metrics.

ClinVar Override Conditions

Override IS applied when:

ClinVar asserts P/LP/B/LB with at least 1 review star

No conflicting computational evidence exists

BA1 does not apply

Override is NOT applied when:

BA1 applies (frequency > 5% always overrides ClinVar)

Conflicting pathogenic + benign evidence exists

ClinVar asserts VUS

Review stars below minimum threshold

Review Stars Explained

StarsMeaning
0Single submitter, no assertion criteria provided
1Single submitter with assertion criteria, or multiple submitters with conflicting interpretations
2Multiple submitters, no conflict, assertion criteria provided
3Reviewed by expert panel
4Practice guideline

Evidence Transparency

When ClinVar classification is used, the criteria string includes "ClinVar" as the first element (e.g., "ClinVar,PM2,PP3") to make the evidence source explicit. The review star level is displayed alongside every variant for the reviewing geneticist to assess assertion quality independently.

Important Caveat

ClinVar assertions vary in quality and may lag behind current evidence. Review star levels indicate the level of review, not the correctness of the assertion. The geneticist should assess ClinVar assertion quality independently, particularly for 0-star and 1-star submissions. The current ClinVar version in production is 2025-01.